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PGM1 P36871

磷酸葡萄糖变位酶-1 (PGM 1) (EC 5.4.2.2) (葡萄糖磷酸变位酶 1)

蛋白质信息 (UniProt)

磷酸葡萄糖变位酶-1 (PGM 1) (EC 5.4.2.2) (葡萄糖磷酸变位酶 1)

P36871

功能描述

催化alpha-D-葡萄糖1-磷酸可逆异构化为alpha-D-葡萄糖6-磷酸 (PubMed:15378030, PubMed:25288802)。该机制通过中间化合物alpha-D-葡萄糖1,6-二磷酸进行 (Probable) (PubMed:25288802)。该enzyme参与葡萄糖的分解和合成 (PubMed:17924679, PubMed:25288802)。 {ECO:0000269|PubMed:15378030, ECO:0000269|PubMed:17924679, ECO:0000269|PubMed:25288802, ECO:0000305|PubMed:15378030}。

亚细胞定位

[Isoform 1]: Cytoplasm.

关键词

3D-structure Acetylation Alternative splicing Carbohydrate metabolism Congenital disorder of glycosylation Cytoplasm Disease variant Glucose metabolism Glycogen storage disease Isomerase