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PEX26 Q7Z412

过氧化物酶体组装蛋白 26 (过氧化物酶体蛋白-26)

蛋白质信息 (UniProt)

过氧化物酶体组装蛋白 26 (过氧化物酶体蛋白-26)

Q7Z412

功能描述

过氧化物酶体锚定因子,将PEX1和PEX6锚定在过氧化物酶体膜上 (PubMed:12717447, PubMed:12851857, PubMed:16257970, PubMed:16763195, PubMed:16854980, PubMed:21362118)。因此,PEX26是形成PEX1-PEX6 AAA ATPase复合物所必需的,该复合物介导PEX5受体从过氧化物酶体膜上的提取 (PubMed:12717447, PubMed:12851857, PubMed:16257970, PubMed:16763195, PubMed:16854980, PubMed:21362118)。 {ECO:0000269|PubMed:12717447, ECO:0000269|PubMed:12851857, ECO:0000269|PubMed:16257970, ECO:0000269|PubMed:16763195, ECO:0000269|PubMed:16854980, ECO:0000269|PubMed:21362118}。

组织特异性

Widely expressed (PubMed:12851857). Highly expressed in kidney, liver, brain and skeletal muscles (PubMed:12851857). Expressed at intermediate level in pancreas, placenta and heart (PubMed:12851857). Weakly expressed in lung (PubMed:12851857).

亚细胞定位

Peroxisome membrane

关键词

Alternative splicing Disease variant Membrane Peroxisome Peroxisome biogenesis disorder Protein transport Proteomics identification Reference proteome Signal-anchor Transmembrane