线粒体tRNA N6-腺苷苏氨酰氨基甲酰转移酶 (EC 2.3.1.234) (N6-L-苏氨酰氨基甲酰腺嘌呤合酶) (t(6)A合酶) (O-唾液酸糖蛋白内肽酶样蛋白1) (OSGEP样蛋白1) (t(6)A37苏氨酰氨基甲酰腺苷生物合成蛋白OSGEPL1) (tRNA苏氨酰氨基甲酰腺苷生物合成蛋白OSGEPL1)
线粒体tRNA N6-腺苷苏氨酰氨基甲酰转移酶 (EC 2.3.1.234) (N6-L-苏氨酰氨基甲酰腺嘌呤合酶) (t(6)A合酶) (O-唾液酸糖蛋白内肽酶样蛋白1) (OSGEP样蛋白1) (t(6)A37苏氨酰氨基甲酰腺苷生物合成蛋白OSGEPL1) (tRNA苏氨酰氨基甲酰腺苷生物合成蛋白OSGEPL1)
Q9H4B0功能描述
Required for the formation of a threonylcarbamoyl group on adenosine at position 37 (t(6)A37) in mitochondrial tRNAs that read codons beginning with adenine. Probably involved in the transfer of the threonylcarbamoyl moiety of threonylcarbamoyl-AMP (TC-AMP) to the N6 group of A37. Involved in mitochondrial genome maintenance. {ECO:0000255|HAMAP-Rule:MF_03179, ECO:0000269|PubMed:29760464, ECO:0000269|PubMed:32047918}.
组织特异性
Widely expressed, with maximum expression in pituitary gland, prostate, rectum and uterus.
亚细胞定位
Mitochondrion
关键词