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BBOX1 O75936

γ-丁基甜菜碱双加氧酶 (EC 1.14.11.1) (γ-丁基甜菜碱羟化酶) (Gamma-BBH) (γ-丁基甜菜碱,2-氧戊二酸双加氧酶)

蛋白质信息 (UniProt)

γ-丁基甜菜碱双加氧酶 (EC 1.14.11.1) (γ-丁基甜菜碱羟化酶) (Gamma-BBH) (γ-丁基甜菜碱,2-氧戊二酸双加氧酶)

O75936

功能描述

催化gamma-butyrobetaine生成L-carnitine。

组织特异性

Highly expressed in kidney; moderately expressed in liver; very low expression in brain.

亚细胞定位

Cytoplasm.

关键词

3D-structure Carnitine biosynthesis Cytoplasm Dioxygenase Iron Metal-binding Oxidoreductase Phosphoprotein Proteomics identification Reference proteome