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ACOX2 Q99424

过氧化物酶体酰基辅酶A氧化酶2 (EC 1.17.99.3) (3-α,7-α,12-α-三羟基-5-β-胆甾烷酰辅酶A 24-羟化酶) (3-α,7-α,12-α-三羟基-5-β-胆甾烷酰辅酶A氧化酶) (三羟基粪甾烷酰辅酶A氧化酶) (THCA-CoA氧化酶) (THCCox)

蛋白质信息 (UniProt)

过氧化物酶体酰基辅酶A氧化酶2 (EC 1.17.99.3) (3-α,7-α,12-α-三羟基-5-β-胆甾烷酰辅酶A 24-羟化酶) (3-α,7-α,12-α-三羟基-5-β-胆甾烷酰辅酶A氧化酶) (三羟基粪甾烷酰辅酶A氧化酶) (THCA-CoA氧化酶) (THCCox)

Q99424

功能描述

氧化胆汁酸中间体二羟基和三羟基胆甾烷酸的CoA酯 (PubMed:27884763)。能够氧化短链和长链2-甲基支链脂肪酸 (By similarity)。 {ECO:0000250|UniProtKB:P07872, ECO:0000269|PubMed:27884763}。

组织特异性

Present in all tissues tested: heart, brain, placenta, lung, liver, skeletal muscle, kidney and pancreas. Most abundant in heart, liver and kidney.

亚细胞定位

Peroxisome

关键词

Direct protein sequencing Disease variant FAD Fatty acid metabolism Flavoprotein Lipid metabolism Oxidoreductase Peroxisome Phosphoprotein Proteomics identification