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PAH P00439

苯丙氨酸-4-羟化酶 (PAH) (EC 1.14.16.1) (Phe-4-单加氧酶)

蛋白质信息 (UniProt)

苯丙氨酸-4-羟化酶 (PAH) (EC 1.14.16.1) (Phe-4-单加氧酶)

P00439

功能描述

催化L-苯丙氨酸羟化为L-酪氨酸。 {ECO:0000269|PubMed:18460651, ECO:0000269|PubMed:18835579}.

关键词

3D-structure Allosteric enzyme Direct protein sequencing Disease variant Iron Metal-binding Monooxygenase Oxidoreductase Phenylalanine catabolism Phenylketonuria