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LTBP2 Q14767

潜伏转化生长因子β结合蛋白2 (LTBP-2)

蛋白质信息 (UniProt)

潜伏转化生长因子β结合蛋白2 (LTBP-2)

Q14767

功能描述

可能在弹性纤维结构组织和/或组装中发挥整体结构作用。 {ECO:0000303|PubMed:10743502, ECO:0000303|PubMed:11104663}.

组织特异性

Expressed in the aorta (at protein level). Expressed in lung, weakly expressed in heart, placenta, liver and skeletal muscle.

亚细胞定位

Secreted, extracellular space, extracellular matrix

关键词

Disease variant Disulfide bond Dwarfism EGF-like domain Extracellular matrix Glaucoma Glycoprotein Growth factor binding Heparin-binding Hydroxylation