3-羟基异丁酰-CoA水解酶, 线粒体 (EC 3.1.2.4) (3-羟基异丁酰辅酶A水解酶) (HIB-CoA水解酶) (HIBYL-CoA-H)
3-羟基异丁酰-CoA水解酶, 线粒体 (EC 3.1.2.4) (3-羟基异丁酰辅酶A水解酶) (HIB-CoA水解酶) (HIBYL-CoA-H)
Q6NVY1功能描述
水解3-羟基异丁酰-CoA (HIBYL-CoA)，一种盐类代谢产物。对异丁酰-CoA具有高活性。可能是一种在缬氨酸代谢中起作用的异丁酰-CoA脱氢酶。也水解3-羟丙酰-CoA。 {ECO:0000269|PubMed:8824301}。
组织特异性
Highly expressed in liver and kidney, also detected in heart, muscle and brain (at protein level). Not detected in lung.
亚细胞定位
Mitochondrion
关键词