GATB O75879

谷氨酰-tRNA(Gln)酰胺转移酶亚基B，线粒体 (Glu-AdT亚基B) (EC 6.3.5.-) (细胞色素c氧化酶组装因子PET112同源物)

蛋白质信息 (UniProt)

谷氨酰-tRNA(Gln)酰胺转移酶亚基B，线粒体 (Glu-AdT亚基B) (EC 6.3.5.-) (细胞色素c氧化酶组装因子PET112同源物)

O75879

功能描述

允许通过线粒体中错误酰化的Glu-tRNA(Gln)的转酰胺作用形成正确负载的Gln-tRNA(Gln)。该反应在谷氨酰胺和ATP存在下，通过活化的γ-磷酸-Glu-tRNA(Gln)进行。 {ECO:0000255|HAMAP-Rule:MF_03147, ECO:0000269|PubMed:19805282}。

组织特异性

Predominantly expressed in tissues characterized by high rates of oxidative phosphorylation (OxPhos), including muscle and heart.

亚细胞定位

Mitochondrion

关键词

ATP-binding Ligase Mitochondrion Nucleotide-binding Primary mitochondrial disease Protein biosynthesis Proteomics identification Reference proteome Transit peptide

外部链接

UniProt: O75879

NCBI Gene

GeneCards